Our Anesthesia Experience in a Patient with Neurofibromatosis

نویسندگان

  • Ozkan Onal
  • Cansu Ciftci
  • Emine Aslanlar
  • Jale Bengi Celik
چکیده

Neurofibromatosis (NF) is an otozomal dominant and multisistemic disorder. Two types were defined: Neurofibromatosis type 1 (NF1) and Neurofibromatosis type 2. Neurofibromas can be found multisystemic and can be cause difficulty for either general anesthesia or regional anesthesia. The patient is 4 years old, 15 kilograms weight, who has common neurofibroms mostly at back and cafe au lait in whole body. She was planned to undergo operation for left inguinal hernia. After 8mg/kg propofol and 2mg/kg fentanyl administration, i-gel was placed and general anesthesia was administered. End of the operation the patient was awakened without any problem. The vital findings of the patient were stable intraoperatively. In postoperative period, no neurological or anesthetical complications occurred and the patients was transferred to the clinic. With this case report, we want to tell anesthesic method in pediatric patient with NF1.

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تاریخ انتشار 2015